Neuro-Behçet’s Disease with Chorea

Neuro-Behçet's Disease with Chorea.

Behçet's disease (BD) was described as a three-symptom complex comprising uveitis, oral aphthae, and genital ulcerations. It is a multisystemic, recurrent, inflammatory disorder and it is of unknown cause. Neuro-Behçet (NB) is present in 5%-7% of BD. Movement disorders have rarely been reported in NB. Here, we report a case of chronic parenchymal NB presenting with chorea.

Neuro-Behçets in a Child

We describe a case of neuro-Behçet disease diagnosed in a 12-year-old girl. This patient presented with recurrent oral ulcers, incontinence, spastic gait, blurry vision, and asymmetrical lower extremity hypertonia. Extensive testing revealed punctate lesions through the central nervous system, vitritis, papillitis, and uveitis. A thorough infectious and neoplastic workup was negative. She was t...

Huntington chorea presenting with motor neuron disease.

BACKGROUND There have been a few case reports of motor neuron disease in association with Huntington disease (HD). OBJECTIVE To describe a patient presenting with prominent fasciculations, chorea, and possible amyotrophic lateral sclerosis (ALS) in whom genetic testing revealed HD mutation. DESIGN Case report. SETTING University of Texas Southwestern Medical Center, Dallas. Patient  A 69-...

Neuro-neutrophilic disease: neuro-Behçet disease and neuro-Sweet disease.

“Neuro-Sweet disease (NSD)” was proposed as a distinct entity of encephalomeningitis in 1999 (1). Sweet disease has been considered as a multisystem inflammatory disorder characterized by painful erythematous plaques, and has been classified as a dermatologic disease. The plaques respond to systemic corticosteroids, and heal without scarring. It has been disclosed that aseptic neutrophilic infl...

Chorea: A Typical Manifestation of Coeliac Disease